Case 1: A neonate with unilateral renal agenesis and a contralateral dysplastic kidney presented with respiratory distress. Prenatal ultrasound revealed severe oligohydramnios, and postnatal imaging confirmed the renal anomalies. The mother was 30 years old with previous history of 2 normal vaginal deliveries.

Case 2: A fetus with bilateral renal agenesis was identified during routine prenatal screening. The ultrasound showed anhydramnios, absent bilateral kidneys. On postmortem evaluation, syndactyly and low set ears were noted. The mother was 30 years old and scan was done at 19 weeks of gestation.

Case 3: A fetus with bilateral renal agenesis and multiple skeletal abnormalities, including limb contractures and flattened facial features, was diagnosed prenatally. Ultrasound also revealed echogenic foci in left ventricle, dilated lateral ventricles, dysplastic humerus and absent radii. Postmortem findings corroborated the diagnosis and revealed additional skeletal anomalies. The mother in this case was 23 years old.

Case 4: A neonate with bladder outlet obstruction and mild oligohydramnios was delivered preterm due to fetal distress. Prenatal ultrasound showed a distended bladder (keyhole sign) and reduced amniotic fluid volume.the bladder outlet obstruction lead to severe palvicocalyceal system dilatation.

In 3 out of 4 cases, there was congenital talipes equinovarus. Dysplastic upper limbs were present in only 1 case out of three. echogenic foci in heart was present in only one case. Absence of kidney lead to low lying adrenals in 3 of 4 cases.