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Congress: ECR25
Poster Number: C-11671
Type: Poster: EPOS Radiologist (educational)
Authorblock: C. Marin Rodriguez, T. Alvarez Martin, A. Lancharro, L. Vara De Andrés, A. Aguado Del Hoyo, M. Sánchez Pérez, Y. Ruiz Martin; Madrid/ES
Disclosures:
Carlos Marin Rodriguez: Nothing to disclose
Teresa Alvarez Martin: Nothing to disclose
Angel Lancharro: Nothing to disclose
Loreto Vara De Andrés: Nothing to disclose
Alejandra Aguado Del Hoyo: Nothing to disclose
María Sánchez Pérez: Nothing to disclose
Yolanda Ruiz Martin: Nothing to disclose
Keywords: Cardiac, Paediatric, CT, MR, Ultrasound, Computer Applications-3D, Contrast agent-intravenous, Congenital, Haemodynamics / Flow dynamics
Learning objectives To review the concept, anatomy and embryology of double outlet right ventricle (DORV). To describe the classification of DORV. To show the clinical manifestations, anatomy, and surgical options for DORV. To highlight the imaging findings that need to be evaluated for appropriate management of DORV and to demonstrate the role of the radiologist in this disease.
Read more Background DORV is an uncommon congenital heart defect, occurring in 0.1% of newborns and representing 1.5% of all congenital heart malformations. It is part of the conotruncal anomalies (malformations of the ventricular outlet) that include Truncus arteriosus and aortopulmonary window Interrupted aortic arch Tetralogy of Fallot (TOF) Transposition of the great arteries DORV The term DORV refers to a group of associated conotruncal anomalies that involve the right ventricular outflow tract, in which both great arteries arise entirely or predominantly from the right ventricle. DORV represents a...
Read more Findings and procedure details DORV with subaortic VSD (VSD type DORV)  In DORV with subaortic VSD oxygenated blood flows from the right ventricle to the pulmonary arteries due to its lower resistance as occurs in usual VSD (Fig.3, video 1) [fig 3] [fig 15] Diagnosis is typically through the use of CUS Advanced imaging may be required in complex cases with associated anomalies (Fig.4) [fig 4] Treatment consists of closure of the VSD using a patch or baffle to redirect from the left ventricle to the aorta. Follow-up of complications can be performed with...
Read more Conclusion DORV is a term used to describe a group of conotruncal anomalies involving the right ventricular outflow tract. In this condition, both great arteries arise entirely or predominantly from the right ventricle.The pathophysiology and treatment of DORV vary depending on the specific type, as outlined in Table [fig 1] .In most cases, preoperative imaging, particularly through CUS, is sufficient. However, in complex cases, particularly those involving the Taussig-Bing anomaly and non-committed VSD type, additional advanced imaging techniques are necessary (see Table II) [fig 2] .Postoperative...
Read more References Obler D, Juraszek AL, Smoot LB, Natowicz MR. Double outlet right ventricle: Aetiologies and associations. Vol. 45, Journal of Medical Genetics. 2008. p. 481–97. Bharucha T, Hlavacek AM, Spicer DE, Theocharis P, Anderson RH. How should we diagnose and differentiate hearts with double-outlet right ventricle? Vol. 27, Cardiology in the Young. Cambridge University Press; 2017. p. 1–15. Ebadi A, Spicer DE, Backer CL, Fricker FJ, Anderson RH. Double-outlet right ventricle revisited. Journal of Thoracic and Cardiovascular Surgery. 2017 Aug 1;154(2):598–604. Villemain O, Belli...
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