Vogt-Koyanagi-Harada syndrome is a rare progressive inflammatory condition of uncertain etiology that affects melanin-containing tissues. Diagnosing this condition is challenging due to a broad differential including infectious and noninfectious causes of uveitis and the lack of a single diagnostic finding on examination, testing, or imaging.VKH It is characterized primarily by chronic bilateral panuveitis, hearing loss, poliosis, vitiligo, and alopecia. The most commonly used imaging test is optical coherence tomography (OCT), but MRI is useful not only for detecting choroidal lesions, as well, but also for indicating labyrinthine, meningeal, and brain parenchymal abnormalities.Choroidal involvement in VKH typically affects both eyes, but around a quarter of patients initially experience unilateral involvement before progressing to bilateral involvement in two weeks. Bilateral choroidal and posterior/retrobulbar thickening and enhancement on Gd-enhanced T1W/FLAIR, and retinal detachment indicating uveitis on MRI, such as leptomeningeal and bilateral labyrinthine membrane enhancement, and high signal on FLAIR in bilateral brain fissures can be present.Recent reports have demonstrated VKH involvement on MRI. They described that leptomeningeal enhancement in VKH may indicate early central nervous system involvement.