The clinical features and disease course of VKH syndrome are well documented. The ultimate revised diagnostic criteria were published in 2022, classifying VKH according to the clinical and ophthalmologic exams, and simplifying diagnostic criteria for acute initial-onset VKH, in which bilateral disease and diffuse choroiditis on EDI-OCT are requirements for the diagnosis of VKH. No alternative methods were provided to confirm bilateral vitritis without those exams. Additional necessary criteria include the absence of prior ocular trauma or surgery, bilateral involvement, and the exclusion of other infectious or inflammatory conditions. Exudative retinal detachment (RD) is a "very helpful criterion," and disc hyperfluorescence along with neurological or auditory findings are "helpful criteria." The role of these "helpful criteria" in diagnosing VKH is not clearly defined, especially for patients who do not meet all of the required criteria. Several studies have illustrated that MRI is valuable in assisting in diagnosing VKH, although MRI findings are not included in the criteria.