Congress:
ECR25
Poster Number:
C-22112
Type:
Poster: EPOS Radiologist (scientific)
DOI:
10.26044/ecr2025/C-22112
Authorblock:
D. Kamal, N. Lamrani, Y. Sijlamassi, N. Moussali, A. Merzem, H. Belgadir, A. Orgi, N. Elbenna, O. Amriss; Casablanca/MA
Disclosures:
Douaa Kamal:
Nothing to disclose
Nadir Lamrani:
Nothing to disclose
Yousra Sijlamassi:
Nothing to disclose
Nadia Moussali:
Nothing to disclose
Aicha Merzem:
Nothing to disclose
Hassna Belgadir:
Nothing to disclose
Anas Orgi:
Nothing to disclose
Naima Elbenna:
Nothing to disclose
Omar Amriss:
Nothing to disclose
Keywords:
Ear / Nose / Throat, CT, MR, Diagnostic procedure, Congenital, Dysplasias
- Cochlear Malformations (50% of cases) [1], [2] :
- Incomplete Partition Type II (IP-II): Most common anomaly (30%), on CT: the basal turn is normal, while these findings affect the middle and apical turns: absent interscalar septum, absent osseous spiral lamina, deficient modiolus. Incomplete partition type II is usually, but not always, associated with the extracochlear findings that contribute to the full Mondini anomaly: large vestibular aqueduct, enlarged vestibule. MR: Care should be taken when interpreting MRI in isolation for cochlear incomplete partition; it should always be correlated to petrous temporal bone CT. T2: on thin sections, absence of interscalar septum and spiral lamina at the level of apical and middle turns may be seen 1
- Common Cavity: Present in 15%, reflecting failure of cochlear and vestibular differentiation. confluence of the cochlea, vestibule and horizontal semicircular canal in a cystic cavity variable in size with no internal architecture. the width of the cavity is typically greater than its height, with the average vertical diameter being 7 mm, and the average horizontal diameter, 10 mm. posterior and superior semicircular canals are absent, normal or malformed. Vestibulocochlear nerve: small or absent components. Facial canal: anomalous course. Ossicles: normal or anomalous stapes, and stenotic oval window. Vestibular aqueduct: not dilated, may be absent
- Cochlear Hypoplasia: Found in 5%, presenting as a smaller than normal cochlea with various internal architectural abnormalities such as having <2 turns. According to the classification of Sennaroglu, there are four radiographically defined types of cochlear hypoplasia. In each type, the cochlea is a structure located at the end of the internal auditory canal, lucent on CT and fluid signal on MRI, that is overall smaller than normal.
- Cochlear Malformations (50% of cases) [1], [2] :
- Incomplete Partition Type II (IP-II): Most common anomaly (30%), on CT: the basal turn is normal, while these findings affect the middle and apical turns: absent interscalar septum, absent osseous spiral lamina, deficient modiolus. Incomplete partition type II is usually, but not always, associated with the extracochlear findings that contribute to the full Mondini anomaly: large vestibular aqueduct, enlarged vestibule. MR: Care should be taken when interpreting MRI in isolation for cochlear incomplete partition; it should always be correlated to petrous temporal bone CT. T2: on thin sections, absence of interscalar septum and spiral lamina at the level of apical and middle turns may be seen 1
- Common Cavity: Present in 15%, reflecting failure of cochlear and vestibular differentiation. confluence of the cochlea, vestibule and horizontal semicircular canal in a cystic cavity variable in size with no internal architecture. the width of the cavity is typically greater than its height, with the average vertical diameter being 7 mm, and the average horizontal diameter, 10 mm. posterior and superior semicircular canals are absent, normal or malformed. Vestibulocochlear nerve: small or absent components. Facial canal: anomalous course. Ossicles: normal or anomalous stapes, and stenotic oval window. Vestibular aqueduct: not dilated, may be absent
- Cochlear Hypoplasia: Found in 5%, presenting as a smaller than normal cochlea with various internal architectural abnormalities such as having <2 turns. According to the classification of Sennaroglu, there are four radiographically defined types of cochlear hypoplasia. In each type, the cochlea is a structure located at the end of the internal auditory canal, lucent on CT and fluid signal on MRI, that is overall smaller than normal.